PHENYLKETONURIA PKU

1
PHENYLKETONURIA (PKU) In Homo sapiens
Extracellular Space
Intracellular Space
Catecholamine biosynthesis
Phenylalanine metabolism
Accumulation
Citric Acid Cycle
Tyrosine metabolism
4-Fumarylacetoacetic acidHMDB01268
Pyridoxal Phosphate
Pyridoxal Phosphate
Pyridoxal Phosphate
Aspartate aminotransferase, cytoplasmic P17174
Tyrosine aminotransferase P17735
Aspartate aminotransferase, cytoplasmic P17174
FAD
  L-amino-acid oxidase Q96RQ9
FAD
  L-amino-acid oxidase Q96RQ9
Pyridoxal Phosphate
Iron
Iron
Homogentisate 1,2-dioxygenase Q93099
Accumulation
Hydroxyphenylpyruvic acid HMDB00707

Homogentisic acidHMDB00130
Phenylpyruvic acid HMDB00205
Iron
4-Hydroxyphenylpyruvate dioxygenase P32754
Accumulation
Phenyllactic acid HMDB00779
Accumulation
Phenyl acetate HMDB01326
Accumulation