Persistent Fetal Vasculature: Management and Results

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Persistent Fetal Vasculature Management and
Results

• Márcia Beatriz Tartarella
• Rodrigo Ueno Takahagi
• Ana Paula Silvério Rodrigues

Federal University of São Paulo
UNIFESP Brasil Head of Congenital Cataract
Service Fellow of Congenital Cataract Service
tartarella_at_hotmail.com
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PURPOSE
Persistent Fetal Vasculature (PFV-PHPV) is a
common congenital developmental anomaly of the
eye that results following failure of the
embryological primary vitreous and hyaloid
vasculature to regress 1-3. It typically presents
unilaterally4 without associated systemic
findings1. PFV can be differentiated into
anterior, posterior and mixed forms, according to
the affected intraocular structures 5-9 .
To describe ocular features, management and
results in patients with persistent fetal
vasculature.
No financial interest
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MATERIALS AND METHODS
A retrospective study in 27 children with
PFV-PHPV was performed. The following data were
analyzed
Sex Age at Diagnosis Systemic Features Birth
History Laterality Clinical Presentation
Axial Length Ecography Ocular Doppler Age at
Surgery Surgery Technique
Visual Acuity Before Surgery Visual Acuity After
Surgery Follow up Period Complication after
Surgery Additional Procedures
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RESULTS

• 14 male x 13 female 29 eyes

Graphic 2.Distribution of patients according to
laterality disease
Graphic 1. Distribution of patients according to
their ages at diagnosis

Graphic 3. Distribution of eyes affected
according to the clinical presentation

  Sistemic feature Patients None
13 Prematurity 4 L
ow weight at birth 8 13 Trissomy 1 CMV mother
infection 1
Table 1. Distribution of patients according to
their sistemic features
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RESULTS

• Microftalmia 14 eyes (58)
• Age at surgery 25 days of life to 3years and
  10 months (mean 14,65 months).

• Surgery 19 eyes (56)

Graphic 4. Distribution of eyes according to the
surgery technique performed

• Follow up period 2 months to 4 years and
  11months ( mean 21 months).

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RESULTS

• Post-op complications 12 eyes (61)

Table 2. Distribution of eyes according to the
complications after surgery
Complication after surgery Eyes None

7 37 Posterior
Sinechiae 5 26.3 Retinal Detachment 5
26.3 Opacification of Posterior
Capsule 3 15.8 Phithisis Bulbi 3
15.8 Pearls over IOL 3
15.8 Leucoma 2 10.5 Pupil membrane 2
10.5

• Additional procedures in 3 eyes 1 Yag laser
  capsulotomy, 1 sinechiae removal and 1 aspiration
  of pearls over IOL.

Graphic 6. Distribution of eyes according to
their visual acuity before and after surgery.
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CONCLUSION PFV-PHPV
Mixed form 80 Lensectomy anterior
vitrectomy 50 Phacoaspiration IOL
21 Phacoaspiration 29 Post operative
complication 61 Surgery is one available
therapy which must be adjusted to patients ocular
features and visual recovering expectation.
Severe complications (26) may be present in the
management of PFV and patients family must be
aware of that.
tartarella_at_hotmail.com
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